ON NOVEMBER 28, the Wall Street Journal published a horrifying article on its front page. Under the headline the u.s. may face mad-cow exposure despite assurances from government, staff writer Steve Stecklow reported that the domestic cattle herd is far from safe, and that the government is doing little to test either cattle or people for signs of illness.
Yet despite Stecklow’s meticulously detailed findings and the story’s prominent placement in one of our most respected newspapers, it pretty much disappeared without a trace. To the extent that any attention has been paid to mad-cow disease during the past month, it was to plug a reassuring report by the Center for Risk Analysis, at the Harvard School of Public Health, that there is vanishingly little likelihood here of a British-style outbreak of mad cow.
What a difference a year makes. In late 2000 and early 2001, network television newscasts and national newsmagazines were filled with terrifying stories about what had happened in Europe, especially in Britain. Cattle in increasing numbers were coming down with bovine spongiform encephalopathy (BSE), a little-understood disease that kills by punching the brain full of tiny holes.
Worse — much worse — was the likelihood that a similar fatal brain disease affecting humans was spreading through the consumption of contaminated beef. The illness was called a " new variant " of a rare condition named Creutzfeldt-Jakob disease, and thus became known, for short, as nvCJD. More than 100 people, nearly all of them from Britain, have died of nvCJD over the past five years.
For the US media, the story was made to order, featuring as it did video of wild-eyed, staggering cows, heaps of burning animal carcasses, distraught farmers, and — in a few cases — footage of twentysomething nvCJD victims trembling through the final stages of their awful disease. " I hate to be blunt, but there was a strong visual to go with it, " says Boston University communications professor Tobe Berkovitz. " A typical science story doesn’t get much play, because you need a visual to be aired ad infinitum or ad nauseam to make it a television news story. And video of shaking, crumbling cows gives you a visual. "
There was, though, a problem with sustaining interest in mad-cow disease. First, there was the inconvenient fact that not a single case of BSE or nvCJD had ever been found in the US. Second, federal officials assured the public that steps taken several years earlier — banning the importation of beef from Britain, and outlawing the use of beef byproducts in animal feed, thought to be the principal means by which BSE is spread — would prevent an outbreak from ever occurring here. By spring, few mad-cow stories were making their way onto the front pages or the network newscasts, as the media turned their attention to more characteristic obsessions. No, it hasn’t disappeared completely — witness a recent episode of The West Wing in which the Bartlet administration debates how best to spin an outbreak of mad cow. But in terms of public consciousness, this is one potential crisis that has faded far into the background.
" There was a period when mad-cow disease was a very telegenic story in an ugly and disturbing sort of way, " says Robert Thompson, director of Syracuse University’s Center for the Study of Popular Television. But then, he notes, " the summer of Gary occurred, and all of a sudden we had all of that time being spent in the cable and broadcast media on Gary Condit and Chandra Levy. " Finally, Thompson observes, " what Gary Condit did to mad cow and some other stories, September 11 did to Gary Condit. "
But if mad-cow disease is, understandably, not as pressing an issue as the hunt for Osama bin Laden, it remains, as the Wall Street Journal article suggests, an important, ongoing story. If mad cow — and, more crucially, nvCJD — breaks out into the US population at some point during the next several years, the media’s chronically short attention span in covering this complicated scientific and medical story will surely stand out as one of their principal failures of 2001.
MAD-COW DISEASE, " classic " (that is, non-nv) CJD, and a similar illness in sheep called scrapie are all known as transmissible spongiform encephalopathies, or TSEs. All of them occur naturally, and scientists believe that mammals, humans included, contract TSEs at the rate of one per million in population. Although the exact cause of TSEs is poorly understood, it is thought by many scientists to be related to the presence of " prions " — proteins that somehow take on a different and deadly shape, and that force other proteins to follow their lead. This process has been compared to " ice-nine, " the substance in Kurt Vonnegut’s 1963 novel Cat’s Cradle that destroys the earth by changing all the water so that it turns solid at room temperature.
Among the best and most thorough treatments of mad-cow disease was an article written for the Atlantic Monthly in 1998 by science journalist Ellen Ruppel Shell. She argues that if BSE arises in cattle naturally at the rate of one in a million, then there would be 100 with BSE among the nation’s 100 million head of cattle at any given time. And if any of those cattle somehow entered the food chain — say, in high-protein animal feed that is later fed back to cattle — then BSE can spread far beyond those 100 head. Humans are exposed by eating contaminated beef — a danger heightened by such practices as slaughtering cattle with pressure guns, which blast highly infectious brain and spinal tissue into the edible parts of the animal carcass.
Shell focuses especially heavily on animal-rendering plants, " a series of altogether unsavory places where dead cats and dogs, road kill, the occasional circus animal, and the diseased carcasses of farm animals are mixed into a ghastly, belching stew. " Yum. Among the products made by these plants is the aforementioned high-protein animal feed, which turns cows into cannibals by feeding them byproducts of other cows — including, potentially, cows with BSE. Complicating this considerably is the fact that other animals dumped into the stew may also have TSEs — especially road kill such as elk and deer, which, in the Western United States, are experiencing an epidemic of a TSE known as chronic wasting disease. Finally, to save on energy costs, rendering plants in recent decades have perfected a system of low-temperature cooking. The problem is that sustained exposure to high temperatures is absolutely essential for killing TSEs.
But if feeding cows to cows is now illegal, well, why should we worry? As it turns out, it’s not nearly that simple. It is still perfectly legal to feed cow byproducts to pigs and chickens, which are not thought to harbor TSEs. And it’s perfectly legal to toss those same pigs and chickens into the rending vats to manufacture feed that can then be fed back to cows. Also, as the Journal article reports, 13 percent of rending plants do not comply with the new regulations against putting beef byproducts into feed intended for cows — and the federal government itself admits that " scores of shipments of animal byproducts for use in animal feed came into the U.S. in recent years from countries that now have mad-cow disease in their cattle herds, a potentially serious source of contamination. "
There is still, though, the simple fact that no cases of BSE or nvCJD have ever been diagnosed in the US. Right? Well, maybe. Some mad-cow specialists say the problem is that the United States has not been inspecting cattle in anywhere near the numbers or with the rigor that British and European authorities now do, meaning that cases of BSE could be slipping by. As for the lack of any human cases, there is at least some reason to believe that there are, in fact, tens of thousands of cases — many of them sitting right in front of us when we visit the nursing home.
In the 1990s, researchers at Yale University and the University of Pittsburgh studied autopsy results of people who had died of Alzheimer’s disease. Although their sample sizes were small, the results were chilling: somewhere between eight and 13 percent were found to have actually had CJD rather than Alzheimer’s. That’s far more than the 250 or so cases that would be statistically expected of " classic, " or naturally occurring, CJD, meaning that a more likely explanation would be the consumption of contaminated meat.
That would also fit with the decades-long incubation period for CJD and nvCJD. According to the Web site of the Alzheimer’s Association, approximately four million Americans have Alzheimer’s — about 10 percent of those who are 65 or older, and nearly half of those who are 85 or older. As Sheldon Rampton and John Stauber wrote in their book Mad Cow U.S.A.: Could the Nightmare Happen Here? (Common Courage, 1997), " If the true number of CJD cases in the United States turns out to be 40,000 instead of 250, the implications for human health would be severe. It could mean that a deadly infectious dementia akin to Britain’s problem has already entered the U.S. population. And since CJD has an invisible latency period of up to 40 years in humans, 40,000 cases could be just the beginning of something much larger. " (A downloadable version of Mad Cow U.S.A. is available for free on the Web site of the Center for Democracy and Technology at http://www.prwatch.org/.)
Ronnie Cummins, national director of the Organic Consumers Association, whose Web site, http://www.purefood.org/, contains an extensive archive of mad-cow information, says that at a minimum the federal government should launch a program of quick, inexpensive tests of both cattle and Alzheimer’s-disease patients to determine whether we may have a hidden mad-cow crisis that warrants further study and action.
" It’s not a question of ‘Do we have mad cow in this country?’ Of course we do, " says Cummins. " Every livestock-grazing country in the world has always had it at low levels. The question is ‘How much do we have, and how quickly is it magnifying?’ "